Rectal Carcinoma in a Young Female Patient with Peutz-Jeghers Syndrome: A Case Report
نویسندگان
چکیده
OBJECTIVE To report a case of rectal cancer in a patient with Peutz-Jeghers syndrome (PJS). CLINICAL PRESENTATION AND INTERVENTION A 20-year-old woman with intermittent bloody stool of 4 months was admitted for examination. Gastroendoscopy revealed multiple polyps involving the stomach, small intestine, colon and a rectal adenocarcinoma. A diagnosis of PJS was made based on intestinal polyps with characteristic pathology and melanotic macules on the lips. After surgery and chemotherapy upon follow-up at 8 months, the patient did not have any signs of recurrence. CONCLUSION This case showed that rectal carcinoma should be considered for young patients with PJS.
منابع مشابه
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عنوان ژورنال:
دوره 23 شماره
صفحات -
تاریخ انتشار 2013